TY - JOUR
T1 - A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle
AU - Raso, Irene
AU - Quarti, Andrea
AU - Chessa, Massimo
AU - Basile, Domenica Paola
AU - Saracino, Antonio
AU - D’Aiello, Angelo Fabio
AU - Raineri, Claudia
AU - Carminati, Mario
AU - Giamberti, Alessandro
N1 - Publisher Copyright:
© The Author(s) 2019.
PY - 2020/5/1
Y1 - 2020/5/1
N2 - Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.
AB - Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.
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U2 - 10.1177/2150135119894292
DO - 10.1177/2150135119894292
M3 - Article
C2 - 32294022
AN - SCOPUS:85147481416
SN - 2150-1351
VL - 11
SP - 358
EP - 360
JO - World Journal for Pediatric and Congenital Heart Surgery
JF - World Journal for Pediatric and Congenital Heart Surgery
IS - 3
ER -